Shrinking Lung Syndrome: A Pulmonary Manifestation of Systemic Lupus Erythematosus

نویسندگان

  • Elsa Naval
  • Christian Domingo
  • Jordi Gratacós
  • Montserrat Bosque
  • Manel Luján
  • Albert Marín
چکیده

Objectives: To describe the diurnal and nocturnal findings of 4 adults (3 women) and one child with systemic lupus erythematosus and shrinking lung syndrome. Design: A prospective observational study. Setting: A 750 teaching-bed-hospital with a reference population of 350,000 people. Interventions: Clinical history, blood analysis, imaging test, pulmonary function tests, maximal inspiratory and expiratory pressures, arterial blood gases, and sleep studies. Measurements and Results: Patients were referred to the pneumology service

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تاریخ انتشار 2004